Extensive lipectomy of Multiple Symmetric Lipomatosis (Madelung’s Disease) |
Dae-in Kim , Jae-hoon Kim , Hee-in Kang , Byung-gwan Moon , Seung-jin Lee , Joo-seung Kim , Deok-ryeong Kim |
Department of Neurosurgery, Eulji General Hospital, Eulji University College of Medicine, Seoul, Korea |
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Abstract |
Multiple symmetric lipomatosis (MSL), also known as Madelung’s disease, is a rare disease characterized by the accumulation of multiple, symmetric, and diffuse nonencapsulated fatty masses around the head, neck, shoulders, and other regions. Although this disease is associated with chronic alcohol abuse, its precise etiology remains unclear. Patients with MSL usually report only cosmetic problems associated with this disease. However, as the masses grow larger and infiltrate deeper into the body, reduced neck mobility or aerodigestive symptoms may occur. The best management strategy for MSL is surgical excision. However, complete excision is often difficult to achieve, since the fatty masses are nonencapsulated and thus diffusely infiltrate the surrounding tissues. Medical treatments and intralesional injections can be used as alternative methods. Here we present one case of MSL treated with surgical excision, which yielded a satisfactory cosmetic result and also alleviated the limitations in neck mobility. This case study has the potential to help doctors as well as surgeons perform accurate diagnosis and proper management of MSL cases. |
Key Words:
LipomatosisㆍMultiple symmetricalㆍLipectomyㆍAlcoholism |
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